Page 121 - Abstract Book KONIKA 18

Cardiology

P-CAR-009
Profile of Congenital Heart Disease in Children with Down Syndrome in
Dr. Chasbullah Abdulmadjid Hospital Bekasi City

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St. Rahmah Rahim , Rosdianah Rahim , Aulia Dadang Nolanda , Tri Yanti Rahayuningsih ,
Mas Wishnuwardhana , Dina Siti Daliyanti , Thommy Harry Adoe , Mira , Charles Antoni , Adrienta 1
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Pediatric Division, Chasbullah Abdulmadjid Hospital Bekasi, West Java , Faculty of Medicine and Health Sciences
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UIN Alauddin Makassar, South Sulawesi , Faculty of Medicine, Universitas Kristen Indonesia, Jakarta , Indonesia
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Abstract
Background Down's syndrome is often accompanied by several disorders, including congenital heart disease
(CHD) which is found in 40-60% of cases and affects the morbidity and mortality rate of children with DS.
Objective To determine the profile of cardiac abnormalities in children with Down syndrome. Methods
This is descriptive retrospective research, exploring secondary data from medical records. The population
in this study were children with Down's Syndrome who came to the pediatric outpatients of Dr. Chassbullah
Abdulmadjid Hospital, Bekasi City from September 2020 to July 2021. Down Syndrome was established
based on physical criteria while the type of heart abnormality was based on the results of echocardiography
performed by a pediatric cardiologist. The data were analyzed using SPSS. Results From 73 DS children,
49 children (67.1%) suffer from CHD with the age mostly range from 12 to 59 months (49%). The highest
classification of CHD was acyanotic CHD (87.8%) with the most type of abnormality being atrial septal
defect (ASD) 42.1%. It was found that 20% of DS children had several type of CHD. Conclusion DS children
have a greater risk being diagnosed from CHD with the most type of abnormality being atrial septal defect.
Cardiac examination should be used as a routine examination in all children with DS.
Keywords: children; Down syndrome; congenital heart disease

P-CAR-010
The Role of Fetal Echocardiography in Congenital Complete Heart Block:
A Case Series of Epicardial Permanent Pacemaker Implantation in Neonates
Winda Azwani, Suprohaita Budyarso, Syarif Rohimi
Department of Child Health, Cardiology Division, PKIAN RSAB Harapan Kita, Jakarta, Indonesia

Abstract
Background The congenital complete heart block (CHB) in the fetus could been detected since 18 week
of gestation.The permanent pacemaker (ppm) implantation in neonatal age is crucial to prevent worsening
heart failure even death. Objective To learn congenital complete heart block management with previous fetal
echocardiography assessment.Case The pregnant mother was referred with fetal bradycardia. Unfortunately,
all five cases came after 28 week of gestation, which transplacental treatment of dexamethasone had no role.
Only one pregnant mother with positive anti-Rho antibodies. The fullterm baby with birthweight between 3070
and 3345 grams have heart rate below 60 beats per minute for all cases. Echocardiography was performed
to rule out major structural heart defect. Electrocardiogram showed complete atrioventricular block for all
subjects. We decided to perform epicardial ppm implantation. In one case, the heart rate decreased below 50
beats per minutes after birth, needed dopamine administration and immediate ppm implantation. The four
cases had heart rate below 60 after dopamine administration. The ppm lead was attached at apex and basal
RV and lateral LV. Only one neonate with posterolateral thoracotomy approach for generator placement,
instead of subxyphoid. Conclusion The prenatal diagnostic of fetal echocardiography has an important role
to plan and parent’s counselling for post-natal outcome.
Keywords: congenital heart block; epicardial permanent pacemaker, fetal echocardiography

KONIKA XVIII Abstract Book 73